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KMID : 0614619930250061337
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Korean Journal of Gastroenterology
1993 Volume.25 No. 6 p.1337 ~ p.1341
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A Case of Intestinal Lymphangiectasia
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전재석
장유현/김태유/류지곤/고광철/미응태/송인성/최규완/김정룡
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Abstract
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intestinal lymphangiectasia is a disorder of small intestine, which is associated with dilation of intestinal lymphatics and leakage from rupture lacteals to intestinal lumen of intestinal lymph which contains plasma proteins, chylomicrons, and
small
lymphocytes. Congenital or primary intestinal lymphangiectasia is due to a malformation of lymphatic systems, whereas secondary intestinal lymphangiectasia is preceded by inflammatory or neoplastic disease and is also caused by decrease in lymph
flow
from thoracic duct due to elevated pressure in the left subclavian vein.
Recently we experienced a 23 year-old female patient with recurrent tetanic attacks and the features of protein-losing enteropathy confirmed by α2-antitrypsin clearance test. And with the aid of blind peroral jejunal biopsy we diagnosed her as
having
intestinal lymphangiectasia, showing dilated lymphatics in the lamina propria. So, we report the first adult case of intestinal lymphangiectasia confirmed by histologic findings in Korea, without apparent secondary cause.
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KEYWORD
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